A case of atypical bovine spongiform encephalopathy (BSE), also known as mad cow disease, has been discovered in a 12-year-old cow in Switzerland's canton of Graubünden. This type of BSE can occur spontaneously and is not linked to the use of animal meal in animal feed. The carcass was incinerated to prevent any risk to other animals or humans, and the meat was not added to the food chain. Despite this finding, Switzerland's international epidemiological status remains unchanged, as atypical BSE cases do not affect the country's negligible BSE risk status, which has been achieved through a ban on animal meal in ruminant feed since 1990.